戻る

発作性夜間血色素尿症（PNH）

関連論文：

		22:	Improvement in the symptoms of smooth muscle dystonia during eculizumab therapy in paroxysmal nocturnal hemoglobinuria.
			著者: Anita Hill, Russell P Rother, Peter Hillmen 雑誌名: Haematologica. 2005 Dec;90(12 Suppl):ECR40. Abstract/Text Aberrant smooth muscle dystonia during hemolytic episodes in paroxysmal nocturnal hemoglobinuria (PNH) is implicated in the symptoms of abdominal pain, dysphagia and erectile dysfunction. Here we report two PNH patients treated with the complement inhibitor, eculizumab. Complement inhibition has been sustained for over 2 years and results in resolution of intravascular hemolysis and amelioration of symptoms associated with smooth muscle contractions. PMID 16464755 Haematologica. 2005 Dec;90(12 Suppl):ECR40.